# DSRCT Models
EWSR1-WT1 Target Genes and Therapeutic Options Identified in a Novel DSRCT In Vitro Model (Cancers) 2021 [https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8657306/](https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8657306/)
Cell models:
JN-DSRCT1
OV-054 DSRCT Cells
### Xenograft, PDX models
SJ-DSRCT PDX1
SJ-DSRCT PDX2
– Nature study 2024
St. Jude Childhood Solid Tumor Network (CSTN) – 6 samples
[Search | Childhood Solid Tumor Network (CSTN) Data Portal | St. Jude Cloud](https://cstn.stjude.cloud/search/)
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|SJDSRCT030490_X1|Desmoplastic small round cell tumor|240|Female|Recurrent, Primary|
|---|---|---|---|---|
|SJDSRCT030722_X1|Desmoplastic small round cell tumor|240|Male|Diagnostic, Metastatic|
|SJDSRCT046151_X1|Desmoplastic small round cell tumor|168|Male|Diagnostic, Primary|
|SJDSRCT046155_X1|Desmoplastic small round cell tumor|276|Male|Recurrent, Primary|
|SJDSRCT049192_X1|Desmoplastic small round cell tumor|132|Male|Diagnostic, Primary|
|SJDSRCT049192_X3|Desmoplastic small round cell tumor|144|Male|Recurrent, Metastatic|
Ewings – SARC0111 PDX model
Ewing Sarcoma Cell Line Atlas website:
[https://hgserver1.amc.nl/cgi-bin/r2/main.cgi?dscope=ESCLA&option=about_dscope](https://hgserver1.amc.nl/cgi-bin/r2/main.cgi?dscope=ESCLA&option=about_dscope)
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[Systematic multi-omics cell line profiling uncovers principles of Ewing sarcoma fusion oncogene-mediated gene regulation: Cell Reports](https://www.cell.com/cell-reports/fulltext/S2211-1247\(22\)01644-8)