# DSRCT Models EWSR1-WT1 Target Genes and Therapeutic Options Identified in a Novel DSRCT In Vitro Model (Cancers) 2021 [https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8657306/](https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8657306/) Cell models: JN-DSRCT1 OV-054 DSRCT Cells ### Xenograft, PDX models SJ-DSRCT PDX1 SJ-DSRCT PDX2 – Nature study 2024 St. Jude Childhood Solid Tumor Network (CSTN) – 6 samples [Search | Childhood Solid Tumor Network (CSTN) Data Portal | St. Jude Cloud](https://cstn.stjude.cloud/search/) ![Pasted image 20250212144741.png](app://5c252e680b863f75c36a0dbce8478de3a732/C:/Obsidian%20(04%2006%202024)/Sam's%20Vault/Pasted%20image%2020250212144741.png?1739332061597) |SJDSRCT030490_X1|Desmoplastic small round cell tumor|240|Female|Recurrent, Primary| |---|---|---|---|---| |SJDSRCT030722_X1|Desmoplastic small round cell tumor|240|Male|Diagnostic, Metastatic| |SJDSRCT046151_X1|Desmoplastic small round cell tumor|168|Male|Diagnostic, Primary| |SJDSRCT046155_X1|Desmoplastic small round cell tumor|276|Male|Recurrent, Primary| |SJDSRCT049192_X1|Desmoplastic small round cell tumor|132|Male|Diagnostic, Primary| |SJDSRCT049192_X3|Desmoplastic small round cell tumor|144|Male|Recurrent, Metastatic| Ewings – SARC0111 PDX model Ewing Sarcoma Cell Line Atlas website: [https://hgserver1.amc.nl/cgi-bin/r2/main.cgi?dscope=ESCLA&option=about_dscope](https://hgserver1.amc.nl/cgi-bin/r2/main.cgi?dscope=ESCLA&option=about_dscope) ![Pasted image 20250212144840.png](app://5c252e680b863f75c36a0dbce8478de3a732/C:/Obsidian%20(04%2006%202024)/Sam's%20Vault/Pasted%20image%2020250212144840.png?1739332120665) [Systematic multi-omics cell line profiling uncovers principles of Ewing sarcoma fusion oncogene-mediated gene regulation: Cell Reports](https://www.cell.com/cell-reports/fulltext/S2211-1247\(22\)01644-8)